The body of each of us normally produces mucus. This fluid substance lines and humidifies the channels of certain organs of our body, and thus allows their protection. In cystic fibrosis, the CFTR protein (Cystic Fibrosis Transmembrane Regulator) responsible for ensuring the fluidity of this mucus does not fulfill its role. The mucus is then thick, sticky and present in large quantities. It is this thick mucus that causes both respiratory and digestive disorders.
- In France, there are approximately 6,500 patients with cystic fibrosis.
- There is 1 newborn affected by the disease every 3 days.
- Cystic Fibrosis affects girls as well as boys